紧急程度低
-中度严重
它是一种影响儿童和青少年的骨癌,主要是高加索人。
它是由遗传改变形成的。它最常见的位置是骨盆和股骨的水平。
它通常在开始时不会引起太多不适,但有时受影响的骨骼会持续数周的疼痛和肿胀,其形状会比另一侧的相同骨骼更大且不同。
对于诊断,有必要进行体检和完整的体检。确认诊断采用互补测试,如X射线,骨活检,骨扫描,计算机断层扫描和磁共振。
应咨询儿科医生或创伤科医生,以扩大研究并指出治疗,通常是手术(越来越不具有侵略性),化疗和放疗。
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- Granowetter L, Womer R, Devidas M, et al. Dose-intensified compared with standard chemotherapy for nonmetastatic Ewing sarcoma family of tumors: a Children's Oncology Group Study. J Clin Oncol 2009; 27:2536.
- Applebaum MA, Worch J, Matthay KK, et al. Clinical features and outcomes in patients with extraskeletal Ewing sarcoma. Cancer 2011; 117:3027.
- Escofet R. Osteosclerosis. Farreras Rozman. Medicina Interna. Volumen 1. 12º edición: 1104.
- Marina N, Granowetter L, Grier HE, et al. Age, Tumor Characteristics, and Treatment Regimen as Event Predictors in Ewing: A Children's Oncology Group Report. Sarcoma 2015; 2015:927123.
医生 Sara Vitoria
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